An Unusual Association of Hyper-IgE Syndrome with Celiac Disease: A Case Report
Ghita Hachim, Jihane El Mahi, Abdelilah Radi, Abdelhakim Ourrai, Rachid Abilkassem, Amal Hassani & Aomar Agadr · Journal of Advances in Medical and Pharmaceutical Sciences · 2022
Hyper-IgE syndrome (HIES) is a primary immunodeficiency disorder characterized by eczema, cold abscesses, pneumonia, eosinophilia, and a very high serum IgE concentration. An association with celiac disease is rare. Immunodeficiency and autoimmunity are two manifestations of immu...