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Laila Benzekri

Publications (7)

Anhidrotic Ectodermal Dysplasia: Report of Two Cases

Narjess Er-rachdy, Ouissal Essadeq, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Background: Anhidrotic ectodermal dysplasia (AED), also referred to as hypohidrotic ectodermal dysplasia, is a rare genetic condition characterized by a triad of hypotrichosis, hypodontia, and hypohidrosis. Case Report: This article reports two illustrative cases: an adolescent a...

Open access Research Article 10.9734/ajpr/2025/v15i7467

Clinical Spectrum of Congenital Ichthyosis in a Moroccan Pediatric Study

Narjess Er-rachdy, Ouissal Essadeq, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Background: Congenital ichthyoses are rare genetic skin disorders characterized by abnormal keratinization, often present at birth and associated with various extracutaneous manifestations. Material and Methods: We conducted a retrospective 30-month study at a Moroccan university...

Open access Research Article 10.9734/ajpr/2025/v15i7464

Clinical Variants of Cutaneous Mastocytosis in Children: Experience from a Single Center

Narjess Er-rachdy, Ouissal Essadeq, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Background: Cutaneous mastocytosis (CM) is a rare pediatric dermatosis characterized by the abnormal proliferation and accumulation of mast cells in the skin. It typically presents in early childhood and is most often confined to the skin, with a generally favorable prognosis. Ma...

Open access Research Article 10.9734/ajpr/2025/v15i7463

Expanding the Spectrum of Hay–wells Syndrome: A Trichoscopic Perspective

Rasha Moumna, Ouissal Essadeq, Ghita Filali Baba, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Aims: Hay–Wells syndrome (ankyloblepharon–ectodermal dysplasia–clefting or AEC syndrome) is a rare autosomal dominant disorder caused by TP63 mutations, classically associated with skin, hair, nail, and craniofacial anomalies. Although hair abnormalities are commonly reported, th...

Open access Research Article 10.9734/ajpr/2025/v15i6455

Unusual Coexistence of Castleman's Disease and Pityriasis Lichenoides in a Child

Narjess Er-rachdy, Ouissal Essadeq, Taha Aaboudech, Kaoutar Znati, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Castleman disease is a rare lymphoproliferative disorder, particularly in children. Its association with pityriasis lichenoides has not been previously reported. This report presents a 5-year-old girl born to consanguineous parents, who developed recurrent necrotic and bullous sk...

Open access Research Article 10.9734/ajpr/2025/v15i7462

Coexistence of Giant Congenital Melanocytic Nevus and Neurofibromatosis Type 1 among Child : A Rare Association

Narjess Er-rachdy, Ouissal Essadeq, Maha Habibi, Taha Aaboudech, Kaoutar Znati, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Background: Giant congenital melanocytic nevus (GCMN) are rare pigmented lesions present at birth, often exceeding 20 cm in size, and may be associated with serious complications such as melanoma and neurocutaneous melanosis. Neurofibromatosis type 1 (NF1) is a common phakomatosi...

Open access Research Article 10.9734/ajpr/2025/v15i8466

Juvenile Lichenoid Mycosis Fungoides: A Rare Variant Case Report with Clinical and Dermoscopic Features

Ouissal Essadeq, Narjess Er-rachdy, Meriem Boubekri, Taha Aaboudech, Kaoutar Znati, Laila Benzekri & Nadia Ismaili · Asian Journal of Pediatric Research · 2025

Background: Lichenoid mycosis fungoides is an exceptionally rare entity in children, often posing significant diagnostic challenges due to its atypical presentation and resemblance to benign dermatoses. Case Report: We report a pediatric case of lichenoid mycosis fungoides presen...

Open access Research Article 10.9734/ajpr/2025/v15i6457