A Rare Case of Mature Cystic Neonatal Sacrococcygeal Teratoma

Abstract

Introduction: Sacrococcygeal teratoma (SCT) is a rare germ cell tumour but the commonest neoplasm during neonatal periods. Aim: We report a rare case of neonatal pure mature cystic sacrococcygeal teratoma (SCT) Type III, who underwent excision of the tumour and coccygectomy, which was the first to be done in Malacca Hospital (a tertiary state hospital in Malacca, Malaysia) since the starting of the paediatric surgery service in the year 2019. Discussion: Postoperatively, the child develops voiding dysfunction due to neurogenic bladder. This was managed by clean intermittent self-catheterisation by the parents and subsequently resolved spontaneously. Histopathological examination revealed that the cyst wall contained all three germ cell lineages, consistent with a pure mature cystic teratoma. Conclusion: Pure mature cystic SCT is rare but benign in nature if diagnosed before the age of 6 months of life and has a good surgical outcome with manageable post-treatment sequelae such as neurogenic bladder and postoperative distinct scar. Surveillance up to at least 5 years is crucial, as it poses the risk of recurrence with potential malignant features.