Management of Dual Diagnosis: Chilaiditi Syndrome and Biliary Atresia Complicated by Cirrhosis

Abstract

Chilaiditi sign is an incidental radiographic finding of a usually asymptomatic condition, where part of the intestine is situated between the liver and the diaphragm. However, the term "Chilaiditi syndrome" is used for symptomatic hepatodiaphragmatic interposition. We report the case of a 15-year-old patient presenting with chronic hepatic colic due to this syndrome, which was diagnosed by abdominal CT scan. Most patients with Chilaiditi syndrome can be managed conservatively. However, surgery is indicated for those who do not respond to conservative management or in cases of suspected serious complications such as ischemia or intestinal perforation. Biliary Atresia (BA) is a rare congenital malformation characterized by an inflammatory and destructive process that obstructs the intra- and extrahepatic bile ducts, leading to rapid progression to complete cholestasis and irreversible biliary cirrhosis, ultimately resulting in the child's death within the first few years of life. Our case is the rare in the literature indicating the association of Chilaiditi syndrome and biliary atresia.