Management of a Bilateral Ectopia Lentis in a Patient with Marfan Syndrome: A Case Report

Abstract

AIMS: to highlight the management procedure of a bilateral subluxated lens in a patient with marfan syndrome. Case Report: We report a case of a 51-year-old woman, with a family history of Marfan syndrome; who presented for a bilateral subluxated lens, iridodonesis and bilateral macular degeneration. Given the family history, the general physical features and the ocular findings, diagnostic of Marfan syndrome was established. The management of the ectopic lentis was very challenging. An intracapsular lens extraction with posterior chamber intraocular lens fixed to the sclera was performed and the patient regained 2/10 visual acuity on the right eye and remained at counting fingers in the left. Conclusion: Marfan syndrome is a rare condition, with various ocular manifestations. The only guarantee for a better visual outcome is a well-designed therapeutic approach.