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Research Article Open access CC BY 4.0

Butterfly-shaped Pattern Dystrophy : Findings of Retinal Imaging

Houda Bezza, Amine Mounsif, Zineb Algouti, Youssef Bennouk, Houssaine Ait Lhaj, Mohamed Kriet, Fouad Elasri

Ophthalmology Research: An International Journal · pp. 26–30 · Published 12 Feb 2024

10.9734/or/2024/v19i1411

Abstract

Butterfly shaped pattern dystophy (BPD) is a inherited macular disease which is characterized by the accumulation of pigment/lipofuscin in the retinal pigment epithelium, it might be misdiagnosed as age-related macular degeneration (AMD). Retinal imaging is a useful tool for the differential diagnosis of pattern dystrophy. In this report, we describe a 64 year old man presented metamorphopsia and reduced visual acuity in both eyes. Fundus examination showed an area of depigmentation delimited resembling a butterfly. The OCT revealed a subfoveal hyperreflective deposit above the retinal pigment epithelium (RPE) while fundus autofluorescence (FAF) shows hypoautofluorescent areas outlined by a lipofuscin deposits as hyperautofluorescent Finally, fluoroscein angiography (FFA) revealed early macular hyperfluorescence. 

Butterfly shaped pattern dystophy macular dytrophy retinal imaging AMD

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