Giant Right Liver Haemangioma Associated with Kasabach-Merritt Syndrome in an Adult Patient

Abstract

Introduction: Liver haemangiomas are often asymptomatic and diagnosed incidentally. Kasabach-Merritt syndrome (KMS) or consumptive coagulopathy is a rare but life-threatening complication of liver haemangioma occurring during observation. Surgery is an appropriate treatment option in such condition and coagulation usually returns to normal after surgical excision. We herein report a case of giant right liver haemangioma with Kasabach-Merritt syndrome treated surgically with literature review. Case Presentation: A 36 –year old woman with a giant liver haemangioma (20 cm) discovered three years ago, who presented to emergency department for pallor and fatigability and no abnormalities were found on physical examination. After excluding haematologic diseases, a Kasabach-Merritt syndrome associated with giant liver haemangioma had been retained. Coagulation disorders returned to normal after successful surgical resection of the lesion by performing a right hepatectomy. Conclusion: Resection is an appropriate and effective surgical procedure to treat giant liver haemangioma associated with Kasabach-Merritt syndrome.